JuniperPublishers-Academic Journal of Pediatrics Neonatology

Juniper Publishers - Journal of Pediatrics Abstract Exomphalos is a rare congenital disorder demonstrated by failure of convergence mesoderm segments. Exomphalos is associated with congenital malformations and chromosomal abnormalities of autosomal or sex chromosomes and abnormalities with increased incidence in various systems such as renal and cardiovascular. The morbidity and mortality can be minimized by recognition of specific abnormalities associated with exomphalos development, the corresponding management and treatment strategies. Conclusion: Exomphalos and umbilical hernias’ may be associated with chromosomal abnormalities in autosomal and sex chromosomes and are related with genetic syndromes such as paternal uniparental disomy (UPD), Pallister-Killian (PKS) and Beckwith-Wiedemann syndrome. Keywords: Exomphalos; Umbicinal hernia; Chromosomal abnormalities; genetic syndromes; Abnormal karyotype Introduction Exompha...

Juniper Publishers - Journal of Pediatrics Abstract Polypoid mass in the prostatic urethra is uncommon but potentially represents a wide spectrum of different entities, ranging from congenital malformations, benign polyps, premalignant disorders to various malignancies. Congenital urethral polyps are rare entity in infancy. They are congenital benign tumors. Most patients present with acute retention, hematuria or intermittent bladder outlet obstruction. The treatmentof choice is transurethral endoscopic ortransvesical resection. Histological study confirms the diagnosis and theprognosis is excellent. We report a case of an 18 month's old boy who presented with acute urinary retention. There was history of dribbling of urine and excessive crying during micturition. Imaging and endoscopic studies confirmed the presence of a polypoid pedunculated lesion at the bladder base arising from posterior urethra. It was excised by cystostomy because of an unsuccessful cys...

Juniper Publishers - Journal of Pediatrics Abstract Complete ureteral duplication with ectopic upper moiety opening into posterior urethra is rare anomalies. This is due to development of two ureteric bud from mesonephric duct. Development of stone in this moiety is rare event. Here we are describing a 12 year old child who presented with left lumbar mass and dysuria. He had left complete duplex ureter with impacted stone at ectopic opening of upper moiety ureter in posterior urethra, simultaneous bladder stone and hydronephrotic non-functioning upper renal moiety. Combined (cystourethroscopy and open surgical) approach was used for management of this case. Keywords: Ectopic ureter; Duplex renal moiety; Stone in duplex kidney Introduction Duplex system can be describes as two pelvicaleceal system with either single lower ureter or double ureter draining into bladder or outside the bladder (ectopic) [ 1 , 2 ]. Duplex system wi...

Juniper Publishers - Journal of Pediatrics Abstract Obstructive fibrinous tracheal pseudomembrane is a rare complication associated with endotracheal intubation. We report the case of a 10-year-old boy hospitalized for a severe abdominal trauma. The boy remained intubated for 4 days. After extubation he started to have stridor and acute respiratory distress so a reintubation was necessary. After 24 hours, an elective extubation was performed and the boy presented stridor and dyspnoea with no improvement with medical treatment. A fibrinous mobile membrane was seen during a flexible bronchoscopy. The pseudomembrane was removed and the patient remained asymptomatic. The knowledge and an early diagnosis of this pathology is very important due to be a life-threatening complication. Introduction Damage of the airways caused by intubation is usually associated with mechanical trauma caused by the endotracheal tube (ETT). Strido...

Juniper Publishers - Journal of Pediatrics Abstract Supraventricular tachyarrhythmia (SVT) is the most common tachyarrhythmia in pediatric patients and accounts for more than 90% of pediatric arrhythmias. As many as 16 different mechanisms of pediatric SVT exist; we focused in this review article on the three most common groups of SVT mechanisms in pediatrics: atrioventricular re-entry tachyarrhythmia (AVRT), atrioventricular nodal re-entry tachyarrhythmia (AVNRT), and a trial tachyarrhythmia (AT). Many methods have been implicated in the diagnosis of SVT like full history taking regarding onset and frequency of palpitation, syncope, chest pain, dispend, heart failure, drug intake and physical examination. Children with suspected SVT must be subjected to resting 12-lead surface ECG and ECG during the attack. Echocardiography must be done for detection of any structural heart diseases. Moreover, recent techniques like Electro physiologic study (EPS) is the most defi...

Juniper Publishers - Journal of Pediatrics Summary Owing to good perinatal care (prenatal detection of problems and timely transport of pregnant women), critically ill newborns are usually delivered in large centres (with tertiary perinatal care provided) where they can be given intensive care and therapy. When this is not the case, a critically ill newborn must be transported to a centre with a higher level of perinatal care. The less time it takes from identifying a problem to transpor to a higher level centre, the better the chances for a better outcome, even though the transport of newborns is still tied to higher morbidity and mortality rates than in utero transport. This is especially the case with extremely preterm and very preterm neonates. The successful medical transport of such high-risk and sensitive population requires a highly specialized personnel and appropriate equipment. In ideal conditions, the neonatal transport team is a link in the system of neo...