Unilateral Complete Ureteral Duplication with Impacted Stone at Ectopic Opening of Upper Moiety Ureter in Posterior Urethra and Simultaneous Bladder Stone: A Rare Entity-Juniper Publishers


Juniper Publishers-Journal of Pediatrics


Abstract

Complete ureteral duplication with ectopic upper moiety opening into posterior urethra is rare anomalies. This is due to development of two ureteric bud from mesonephric duct. Development of stone in this moiety is rare event. Here we are describing a 12 year old child who presented with left lumbar mass and dysuria. He had left complete duplex ureter with impacted stone at ectopic opening of upper moiety ureter in posterior urethra, simultaneous bladder stone and hydronephrotic non-functioning upper renal moiety. Combined (cystourethroscopy and open surgical) approach was used for management of this case.
Keywords: Ectopic ureter; Duplex renal moiety; Stone in duplex kidney


Introduction

Duplex system can be describes as two pelvicaleceal system with either single lower ureter or double ureter draining into bladder or outside the bladder (ectopic) [1,2]. Duplex system with double ureter and ectopic opening of upper pole ureter into proximal urethra (ectopic) is rare anomalies compare to bifid ureter [1]. Stone formation in duplex system is potential complication [1,3-5]. Combined approach should be used to deal such situation in resource poor setting.


Case Report

Twelve year old male child presented with complain of colicky pain with mass in left lumbar region and dysuria since 5 month. No history of fever, hematuria or trauma to abdomen. Examination revealed single 10cm x 8cm nontender cystic ballotable mass in left lumbar region. Complete blood count was normal, urea 32mg%, creatinine 0.6mg% Ca 9mg% uric acid 5.6mg% PO4 5.3mg%, urine microscopy 25 pus cells/HPF, urine culture no growth, Plain X-ray shows two radiopaque shadow in pelvis (Figure 1), USG shows Right kidney Normal, Left upper moiety gross hydronephrotic, left ureter dilated till lower end, lower moiety normal, Stone in urinary bladder (1.5cm) and Left VUJ (1.6cm). Intravenous urogram (IVU) and nuclear imaging suggestive of left upper moiety nonfunctioning (Figure 2 & 3), left lower moiety normal. Right kidney normal.
During cystourethroscopy one stone was impacted at ectopic opening of ureter and projecting into posterior urethra in curvilinear fashion and another stone in urinary bladder, stone at ectopic opening was disimpacted and pushed backed into ureter and child was catheterized. Open left upper pole nephrouretectomy with removal of ureteral stone and cystolithotomy was performed.
Figure 4 (specimen) showing stone of urinary bladder (upper) and impacted stone of ectopic ureter (red arrow). Post operatively child recovers well and on 6 month follow up child was well.


Discussion

Duplex system with double ureter with ectopic opening of upper moiety ureter into posterior urethra in male child is rare anomalies [1,6]. In duplex system lower moiety is usually good functioning and upper moiety having ectopic opening of ureter is hydronephrotic and poor or nonfunctioning [7,8], as in our case. Ureteral duplication with ectopic upper moiety ureter in male child is usually asymptomatic. These duplex systems are vulnerable for urinary tract infections and urolithiasis. Urinary calculi are often due to relative stasis of urine but may occur due to factors unrelated to the duplication. Development of stone in upper moiety ureter may be due to either obstruction, recurrent infection or other factor. Treatment of nonfunctioning upper moiety is surgical removal [7].
Retrieval of large stone per urethrally is difficult task in setting where lithotripter is not available. In this case we had to disimpact and push backed the stone into the ureter so that we could be able to remove stone by open surgery

Duplex moiety with impacted stone in lower end of upper moiety ureter can be dealed with combined approach (cystoscopy and open) in resource poor setting.

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